The prognosis for people with SWS is directly related to the amount of brain involvement for the leptomeningeal angiomas. For those individuals with smaller angiomas, prognosis is relatively good.
Port-wine stains are present at birth, and seizures may occur in early childhood. If an individual has both of these features, SWS should be suspected.
Males are affected with Bassen-Kornzweig syndrome with greater frequency (70%) than girls, which is uncharacteristic in most autosomal recessive conditions.
As with other types of spinal cord injuries, men are more frequently affected by central cord syndrome than women. In younger individuals (secondary to trauma) or in older individuals (secondary to...