After two weeks the normal jaundice of the newborn will not disappear.the stools will probably be clay-colored.the child's abdomen will begin to swell.Nearly all untreated children will die of liver failure within two years.
some may develop a bluish complexion (cyanosis), caused by a lack of sufficient oxygen in the circulatory system. The infant's abdomen may be distended (swollen and firm
Biliary drainage can usually be established, but the patients still have a defective biliary system that develops progressive disease.Transplantation now achieves up to 90% one-year survival rates...